---
title: "ICD-10-CM E78.9: Disorder of lipoprotein metabolism… | BillingBrief"
description: "ICD-10-CM code E78.9: Disorder of lipoprotein metabolism, unspecified. Category, related codes, and the official source, in plain English."
canonical: "https://billingbrief.com/icd10/e78.9/"
language: "en"
---

# E78.9 Disorder of lipoprotein metabolism, unspecified

ICD-10-CM · [CMS code reference](#source)

**Official ICD-10-CM description:** Disorder of lipoprotein metabolism, unspecified

## Coding notes

From the ICD-10-CM FY2027 (effective October 1, 2026) tabular list. Notes on a parent code or category apply here too.

### Excludes1

Not coded together with this code. The exception is when the two conditions are unrelated to each other.

-   sphingolipidosis (E75.0-E75.3)
-   androgen insensitivity syndrome (E34.5-)
-   congenital adrenal hyperplasia (E25.0)
-   hemolytic anemias attributable to enzyme disorders (D55.-)
-   Marfan syndrome (Q87.4-)
-   5-alpha-reductase deficiency (E29.1)

### Excludes2

Not part of this code, but both can be coded when both are documented.

-   Ehlers-Danlos syndromes (Q79.6-)

## Related codes

-   [`E78.5` Hyperlipidemia, unspecified ICD-10-CM](https://billingbrief.com/icd10/e78.5/)
-   [`E78.6` Lipoprotein deficiency ICD-10-CM](https://billingbrief.com/icd10/e78.6/)
-   [`E78.70` Disorder of bile acid and cholesterol metabolism, unspecified ICD-10-CM](https://billingbrief.com/icd10/e78.70/)
-   [`E78.71` Barth syndrome ICD-10-CM](https://billingbrief.com/icd10/e78.71/)
-   [`E78.72` Smith-Lemli-Opitz syndrome ICD-10-CM](https://billingbrief.com/icd10/e78.72/)
-   [`E78.79` Other disorders of bile acid and cholesterol metabolism ICD-10-CM](https://billingbrief.com/icd10/e78.79/)
-   [`E78.81` Lipoid dermatoarthritis ICD-10-CM](https://billingbrief.com/icd10/e78.81/)
-   [`E78.89` Other lipoprotein metabolism disorders ICD-10-CM](https://billingbrief.com/icd10/e78.89/)

## Common questions

### Is E78.9 a billable code?

Yes. E78.9 is a billable ICD-10-CM code in the ICD-10-CM FY2027 (effective October 1, 2026) code set.

## From the source

Official description from [CMS](https://www.cms.gov/medicare/coding-billing/icd-10-codes).
ICD-10-CM FY2027 (effective October 1, 2026).

Code set

ICD-10-CM

Category

E78 Disorders of lipoprotein metabolism and other lipidemias

Chapter

Endocrine, nutritional and metabolic diseases

Billable

Yes

Educational reference only. Not medical, legal, or billing advice. Always check the current official code set and payer policy before you bill. [About BillingBrief and our sources](https://billingbrief.com/about/).